Hyperparathyroidism-jaw tumor syndrome

Orpha code: 99880OMIM code: 145001

Definition

A rare genetic disease characterized by synchronous or metachronous occurrence of primary hyperparathyroidism and ossifying fibroma of the maxilla and/or mandible, associated with an increased risk of parathyroid carcinoma. Occurrence of renal cysts or tumors, multiple uterine polyps, and thyroid tumors has also been reported.

Disease data
Classification

Disease

Synonyms
HPT-JT
HPT-JT
ORPHA code
99880
OMIM code
145001
ICD10 code
E21.0
ICD11 code
-

No additional description.

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