Turcot syndrome with polyposis

Orpha code: 99818OMIM code: 175100

Definicja

Turcot syndrome with polyposis or Turcot syndrome type 2 is a form of familial adematous polyposis, characterized by the concurrence of thousands of colonic adenomatous polyposis or colorectal cancer (CRC) and a primary central nervous system tumor (principally medulloblastoma). It is also associated with pigmented ocular fundus lesions.

Disease data
Klasyfikacja

Clinical subtype

Kod ORPHA
99818
Kod OMIM
175100
Kod ICD10
D12.6
Kod ICD11
-

No additional description.

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