Dentin dysplasia-sclerotic bones syndrome

Orpha code: 99792OMIM code: 125440

Definition

Dentin dysplasia-sclerotic bones syndrome is a rare, genetic odontologic disease characterized by the clinical, radiographic, and histologic features of dentine dysplasia and osteosclerosis of all long bones, with heavy cortical bone and narrowed or occluded marrow spaces. There have been no further descriptions in the literature since 1977.

Disease data
Classification

Disease

ORPHA code
99792
OMIM code
125440
ICD10 code
K00.5
ICD11 code
-

No additional description.

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