Cheirospondyloenchondromatosis

Orpha code: 99647OMIM code:

Definicja

Cheirospondyloenchondromatosis is an extremely rare type of enchondromatosis of very early onset (from neonatal period to infancy) characterized by symmetrical multiple enchondromas with metacarpal and phalangeal involvement resulting in short hands and feet, platyspondyly, mild to moderate short stature and intellectual disability.

Disease data
Klasyfikacja

Disease

Synonimy
Generalized enchondromatosis with platyspondyly
Generalized enchondromatosis with platyspondyly
Kod ORPHA
99647
Kod OMIM
-
Kod ICD10
Q78.8
Kod ICD11
-

No additional description.

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