Coronary sinus stenosis

Orpha code: 99117OMIM code:

Definition

A rare congenital anomaly of the coronary sinus characterized by its stenosis at the ostium, lumen, or origin, typically leading to dilation of the vessel. Symptoms are variable and can include palpitations, tachypnea, dyspnea, chest pain, fatigue, and cyanosis. The malformation may be associated with other cardiac anomalies, such as coronary artery-coronary sinus fistula, unroofed coronary sinus, atrial septal defect, coronary sinus-left atrium fistula, total anomalous pulmonary venous connection, and ventricular septal defect.

Disease data
Classification

Morphological anomaly

ORPHA code
99117
OMIM code
-
ICD10 code
Q21.1
ICD11 code
-

No additional description.

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