Primary dystonia, DYT13 type

Orpha code: 98807OMIM code: 607671

Definition

A rare primary torsion dystonia characterized by focal or segmental dystonia with onset either in the cranial-cervical region or in the upper limbs. Age of onset varies between 5 years and adulthood, with a mean age of onset of 16 years. Clinical manifestations are generally mild and slowly progressive.

Disease data
Classification

Disease

Synonyms
DYT13
Primary dystonia with mixed phenotype
Primary torsion dystonia with predominant craniocervical or upper limb onset
DYT13
Primary dystonia with mixed phenotype
Primary torsion dystonia with predominant craniocervical or upper limb onset
ORPHA code
98807
OMIM code
607671
ICD10 code
G24.1
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl