Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare renal disease characterized by congenital unilateral or bilateral narrowing of the renal artery leading to severe arterial hypertension and progressive renal failure in the neonate. Manifestations include hypertensive encephalopathy and/or neurological signs and symptoms due to hyponatremia, polyuria, renal electrolyte loss, proteinuria, and hematuria. Disease data Classification Disease Synonyms Congenital renovascular hypoplasia Wrodzona hipoplazja nerkowo-naczyniowa ORPHA code 97598 OMIM code - ICD10 code Q27.1 ICD11 code LA90.40 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl