Congenital renal artery stenosis

Orpha code: 97598OMIM code:

Definicja

A rare renal disease characterized by congenital unilateral or bilateral narrowing of the renal artery leading to severe arterial hypertension and progressive renal failure in the neonate. Manifestations include hypertensive encephalopathy and/or neurological signs and symptoms due to hyponatremia, polyuria, renal electrolyte loss, proteinuria, and hematuria.

Disease data
Klasyfikacja

Disease

Synonimy
Congenital renovascular hypoplasia
Wrodzona hipoplazja nerkowo-naczyniowa
Kod ORPHA
97598
Kod OMIM
-
Kod ICD10
Q27.1
Kod ICD11
LA90.40

No additional description.

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