Multiloculated renal cyst

Orpha code: 97366OMIM code:

Definition

A rare benign renal tumor characterized by a typically unilateral, solitary, multiloculated cystic mass consisting of small, non-communicating cysts with flat, cuboidal, or hobnail epithelial lining, separated by fibrous septa which may have an ovarian stroma-like appearance or be paucicellular. The tumor is surrounded by a thick fibrous capsule and does not contain solid areas or necrosis. Patients may be asymptomatic or present with a palpable abdominal mass and/or abdominal or flank pain. Age distribution is bimodal, the typical age of onset being either below five or between 40 and 70 years of age.

Disease data
Classification

Morphological anomaly

Synonyms
Multilocular cyst of the kidney
Wielokomorowa torbiel nerki
Multilocular renal cyst
ORPHA code
97366
OMIM code
-
ICD10 code
-
ICD11 code
-

No additional description.

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