Wielokomorowa torbiel nerki

Kod Orpha: 97366Kod OMIM:

Definicja

A rare benign renal tumor characterized by a typically unilateral, solitary, multiloculated cystic mass consisting of small, non-communicating cysts with flat, cuboidal, or hobnail epithelial lining, separated by fibrous septa which may have an ovarian stroma-like appearance or be paucicellular. The tumor is surrounded by a thick fibrous capsule and does not contain solid areas or necrosis. Patients may be asymptomatic or present with a palpable abdominal mass and/or abdominal or flank pain. Age distribution is bimodal, the typical age of onset being either below five or between 40 and 70 years of age.

Dane
Klasyfikacja

Wada morfologiczna

Synonimy
Multilocular cyst of the kidney
Wielokomorowa torbiel nerki
Multilocular renal cyst
Kod ORPHA
97366
Kod OMIM
-
Kod ICD10
D30.0
Kod ICD11
-

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