Thymic neuroendocrine tumor

Orpha code: 97289OMIM code:

Definition

A rare, malignant, primary thymic neoplasm originating from neuroendocrine cells, presenting as a mass within the anterior mediastinum. Patients typically present with nonspecific symptoms, such as chest pain, cough, shortness of breath, or in some cases, superior vena cava syndrome, although patients could be asymptomatic during the early stages or present with multiple endocrine neoplasia type I. Ectopic production of ACTH and serotonin can lead to Cushing syndrome and carcinoid syndrome, respectively.

Disease data
Classification

Disease

ORPHA code
97289
OMIM code
-
ICD10 code
C37
ICD11 code
-

No additional description.

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