Glycogen storage disease due to phosphoglycerate mutase deficiency

Orpha code: 97234OMIM code: 261670

Definition

A rare metabolic myopathy characterized by exercise-induced cramp, myoglobinuria, and presence of tubular aggregates in the muscle biopsy. Serum creatine kinase (CK) levels are increased between episodes of myoglobinuria.

Disease data
Classification

Disease

Synonyms
GSD due to phosphoglycerate mutase deficiency
Glikogenoza z powodu niedoboru mutazy fosfoglicerynianu
GSD typu 10
GSD z powodu niedoboru mutazy fosfoglicerynianu
Miopatia z powodu niedoboru mutazy fosfoglicerynianu
Niedobór mięśniowej mutazy fosfoglicerynianu
GSD type 10
Glycogenosis due to phosphoglycerate mutase deficiency
Muscle phosphoglycerate mutase deficiency
Myopathy due to phosphoglycerate mutase deficiency
ORPHA code
97234
OMIM code
261670
ICD10 code
E74.0
ICD11 code
-

No additional description.

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