12q14 microdeletion syndrome

Orpha code: 94063OMIM code:

Definition

12q14 microdeletion syndrome is characterised by mild intellectual deficit, failure to thrive, short stature and osteopoikilosis. It has been described in four unrelated patients. The syndrome appears to be caused by a heterozygous deletion at chromosome region 12q14, which was detected in three of the four patients. The deleted region contains the <i>LEMD3</i> gene: mutations in this gene have already been implicated in osteopoikilosis.

Disease data
Classification

Malformation syndrome

Synonyms
Del(12)(q14)
Del(12)(q14)
Delecja 12q14
Monosomia 12q14
Osteopoikilia - niski wzrost - niepełnosprawność intelektualna
Deletion 12q14
Monosomy 12q14
Osteopoikilosis-short stature-intellectual disability syndrome
ORPHA code
94063
OMIM code
-
ICD10 code
Q93.5
ICD11 code
-

No additional description.

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