Immune-mediated thrombotic thrombocytopenic purpura

Orpha code: 93585OMIM code:

Definition

A rare, non-hereditary thrombotic thrombocytopenic purpura (TTP), characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and single or multiple organ failure of variable severity.

Disease data
Classification

Clinical subtype

Synonyms
Acquired TTP
Autoimmunologiczna plamica zakrzepowa małopłytkowa
Nabyta TTP
Acquired thrombotic thrombocytopenic purpura
Autoimmune thrombotic thrombocytopenic purpura
Thrombotic thrombocytopenic purpura due to anti-ADAMTS-13 antibodies
aTTP
iTTP
ORPHA code
93585
OMIM code
-
ICD10 code
M31.1
ICD11 code
-

No additional description.

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