Syndactyly type 4

Orpha code: 93405OMIM code: 186200

Definicja

A rare non-syndromic syndactyly characterized by complete bilateral cutaneous fusion of all fingers, frequently associated with polydactyly (usually involving six digits and six metacarpals). Phalanges may fuse as a conglomerate mass of bones. Feet are occasionally affected.

Disease data
Klasyfikacja

Morphological anomaly

Synonimy
Polysyndactyly, Haas type
Polisyndaktylia, typ Haasa
Kod ORPHA
93405
Kod OMIM
186200
Kod ICD10
Q70.4
Kod ICD11
-

No additional description.

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