Spondyloepimetaphyseal dysplasia, PAPSS2 type

Orpha code: 93282OMIM code: 612847

Definition

Spondyloepimetaphyseal dysplasia (SEMD), Pakistani type is characterized by short stature, short and bowed lower limbs, mild brachydactyly, kyphoscoliosis, abnormal gait, enlarged knee joints, precocious osteoarthropathy, and normal intelligence.

Disease data
Classification

Disease

Synonyms
Spondyloepimetaphyseal dysplasia, Pakistani type
Spondyloepimetaphyseal dysplasia, Pakistani type
ORPHA code
93282
OMIM code
612847
ICD10 code
Q77.7
ICD11 code
-

No additional description.

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