Centrifugal lipodystrophy

Orpha code: 90156OMIM code:

Definition

Centrifugal lipodystrophy is a rare, acquired, localized lipodistrophy characterized by single or, occasionally, multiple, centrifugally progressive, asymptomatic to sometimes mildly tender, hypopigmented, lipoatrophic skin depressions with weakly erymatheous inflammatory borders, typically associated with regional ipsilateral lymph nodes swelling. Lesions typically occur on lower trunk (in particular groin and abdomen region), followed by upper trunk (axilla and neighboring regions) and, rarely, neck and head. It is usually not associated with systemic disease and is typically self-resolving.

Disease data
Classification

Disease

Synonyms
Lipodystrophia centrifugalis abdominalis infantilis
Lipodystrophia centrifugalis abdominalis infantilis
ORPHA code
90156
OMIM code
-
ICD10 code
E88.1
ICD11 code
-

No additional description.

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