Lipodystrofia odśrodkowa

Kod Orpha: 90156Kod OMIM:

Definicja

Centrifugal lipodystrophy is a rare, acquired, localized lipodistrophy characterized by single or, occasionally, multiple, centrifugally progressive, asymptomatic to sometimes mildly tender, hypopigmented, lipoatrophic skin depressions with weakly erymatheous inflammatory borders, typically associated with regional ipsilateral lymph nodes swelling. Lesions typically occur on lower trunk (in particular groin and abdomen region), followed by upper trunk (axilla and neighboring regions) and, rarely, neck and head. It is usually not associated with systemic disease and is typically self-resolving.

Dane
Klasyfikacja

Choroba

Synonimy
Lipodystrophia centrifugalis abdominalis infantilis
Lipodystrophia centrifugalis abdominalis infantilis
Kod ORPHA
90156
Kod OMIM
-
Kod ICD10
E88.1
Kod ICD11
EF01.1

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