Inflammatory pseudotumor of the liver

Orpha code: 90003OMIM code:

Definition

A rare benign liver tumor characterized by a prominent inflammatory infiltrate and often mimicking a malignant liver neoplasm. The tumor is frequently solitary with a predilection for the right lobe; however, multiple lesions are possible. There are two clinicopathological subtypes: fibrohistiocytic inflammatory pseudotumor of the liver and lymphoplasmacytic inflammatory pseudotumor of the liver. Patients present with non-specific clinical symptoms such as abdominal pain or discomfort, fever, and weight loss. The condition may be associated with other chronic inflammatory or autoimmune diseases.

Disease data
Classification

Disease

ORPHA code
90003
OMIM code
-
ICD10 code
K75.8
ICD11 code
-

No additional description.

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