Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A clonal B-cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains. It usually presents as systemic AL amyloidosis with involvement of one or more parenchymal organ(s) and, less frequently, as localized amyloidosis with usually nodular deposits restricted to a single organ and/or system. Disease data Classification Disease Synonyms Light-chain amyloidosis Amyloidoza immunoglobulinowa Amyloidoza łańcuchów lekkich Amyloidoza pierwotna Primary amyloidosis ORPHA code 85443 OMIM code 254500 ICD10 code E85.9 ICD11 code 5D00.0 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl