Genitopatellar syndrome

Orpha code: 85201OMIM code: 606170

Definition

Genitopatellar syndrome is a rare congenital patellar anomaly syndrome characterized by patellar aplasia or hypoplasia associated with microcephaly, characteristic coarse facial features (microcephaly, bitemporal narrowing, large, broad nose with high nasal bridge, prominent cheeks and micro/retrognathia or prognathism), arthrogryposis of the hips and knees, urogenital abnormalities and intellectual deficiency.

Disease data
Classification

Malformation syndrome

Synonyms
Absent patellae-scrotal hypoplasia-renal anomalies-facial dysmorphism-intellectual disability syndrome
Brak rzepki - hipoplazja moszny - wady nerek - dysmorfia twarzy - niepełnosprawność intelektualna
ORPHA code
85201
OMIM code
606170
ICD10 code
Q87.8
ICD11 code
-

No additional description.

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