Proximal spinal muscular atrophy type 4

Orpha code: 83420OMIM code: 271150

Definition

A rare, genetic proximal spinal muscular atrophy characterized by degeneration of alpha motor neurons in the anterior horns of the spinal cord and lower brain stem manifesting with adult onset, slowly progressive, mild proximal muscle weakness.

Disease data
Classification

Clinical subtype

Synonyms
SMA type 4
Rdzeniowy zanik mięśni, postać dorosła
SMA typu 4
SMA typu IV
SMA4
SMA-IV
SMA type IV
SMA-IV
SMA4
Spinal muscular atrophy, adult form
ORPHA code
83420
OMIM code
271150
ICD10 code
G12.1
ICD11 code
8B61.3

No additional description.

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