Methylmalonic acidemia with homocystinuria type cblF

Orpha code: 79284OMIM code: 277380

Definition

<i>cblF</i> type methylmalonic acidemia with homocystinuria is a form of methylmalonic acidemia with homocystinuria (see this term), an inborn error of vitamin B12 (cobalamin) metabolism characterized by megaloblastic anemia, lethargy, failure to thrive, developmental delay, intellectual deficit and seizures.

Disease data
Classification

Clinical subtype

Synonyms
CblF defect
Acyduria metylomalonowa z homocystynurią, type cblF
Defekt CblF
Defekt kobalaminy F
Niedobór lizosomalnego transportera błonowego kobalaminy
Złożony defekt syntezy adenozylkobalaminy i metylkobalaminy, typu cblF
Cobalamin F defect
Combined defect in adenosylcobalamin and methylcobalamin synthesis, type cblF
Lysosomal membrane cobalamin transporter deficiency
Methylmalonic aciduria with homocystinuria, type cblF
ORPHA code
79284
OMIM code
277380
ICD10 code
E72.1
ICD11 code
-

No additional description.

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