Methylmalonic acidemia with homocystinuria, type cblD

Orpha code: 79283OMIM code: 277410

Definition

<i>cblD</i> type methylmalonic acidemia with homocystinuria is a form of methylmalonic acidemia with homocystinuria (see this term), an inborn error of vitamin B12 (cobalamin) metabolism characterized by variable biochemical, neurological and hematological manifestations.

Disease data
Classification

Clinical subtype

Synonyms
CblD defect
Acyduria metylomalonowa z homocystynurią, typu cblD
Defekt CblD
Defekt kobalaminy D
Złożony defekt syntezy adenozylkobalaminy i metylkobalaminy, typu cblD
Cobalamin D defect
Combined defect in adenosylcobalamin and methylcobalamin synthesis, type cblD
Methylmalonic aciduria with homocystinuria, type cblD
ORPHA code
79283
OMIM code
277410
ICD10 code
E72.1
ICD11 code
-

No additional description.

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