Methylmalonic acidemia with homocystinuria, type cblC

Orpha code: 79282OMIM code: 277400

Definition

<i>cblC</i> type methylmalonic acidemia with homocystinuria is a form of methylmalonic acidemia with homocystinuria (see this term), an inborn error of vitamin B12 (cobalamin) metabolism characterized by megaloblastic anemia, lethargy, failure to thrive, developmental delay, intellectual deficit and seizures.

Disease data
Classification

Clinical subtype

Synonyms
CblC defect
Acyduria metylomalonowa z homocystynurią, typu cblC
Defekt CblC
Defekt kobalaminy C
Złożony defekt syntezy adenozylkobalaminy i metylkobalaminy, typu cblD
Cobalamin C defect
Combined defect in adenosylcobalamin and methylcobalamin synthesis, type cblC
Methylmalonic aciduria with homocystinuria, type cblC
ORPHA code
79282
OMIM code
277400
ICD10 code
D58.8
ICD11 code
-

No additional description.

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