Infantile neuronal ceroid lipofuscinosis

Orpha code: 79263OMIM code: 256730

Definition

Infantile neuronal ceroid lipofuscinosis (INCL) is a form of neuronal ceroid lipofuscinosis (NCL; see this term) characterized by onset during the second half of the first year of life and rapid mental and motor deterioration leading to loss of all psychomotor abilities.

Disease data
Classification

Disease

Synonyms
Hagberg-Santavuori disease
Choroba Hagberga i Santavuori
Choroba Santavuori
Choroba Santavuori i Haltia
INCL
NCL dziecięca
INCL
Infantile NCL
Santavuori disease
Santavuori-Haltia disease
ORPHA code
79263
OMIM code
256730
ICD10 code
E75.4
ICD11 code
-

No additional description.

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