Pyruvate dehydrogenase E2 deficiency

Orpha code: 79244OMIM code: 245348

Definicja

A very rare form of pyruvate dehydrogenase deficiency (PDHD) characterized by variable lactic acidosis and neurological dysfunction, mainly appearing during childhood.

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex deficiency
Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex deficiency
Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex deficiency
Niedobór dehydrogenazy pirogronianowej kompleksu komponentu E2
Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex deficiency
Pyruvate dehydrogenase complex component E2 deficiency
Kod ORPHA
79244
Kod OMIM
245348
Kod ICD10
E74.4
Kod ICD11
-

No additional description.

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