Atrophoderma vermiculata

Orpha code: 79100OMIM code: 604093

Definicja

A rare genetic skin disease characterized by childhood onset of follicular keratotic papules slowly progressing to characteristic ''honeycomb'' atrophy on the cheeks, preauricular area, and forehead. Less frequently, the condition may affect also the upper lip, ears, or limbs. Additional features include facial erythema, milia, and follicular plugs.

Disease data
Klasyfikacja

Disease

Synonimy
Folliculitis ulerythematosa reticulate
Rogowacenie zapalne mieszków włosowych siatkowate
Kod ORPHA
79100
Kod OMIM
604093
Kod ICD10
L66.4
Kod ICD11
ED56

No additional description.

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