Tropical endomyocardial fibrosis

Orpha code: 75565OMIM code:

Definition

Tropical endomyocardial fibrosis is a restrictive cardiopathy, occuring almost exclusively in children and young adults in tropical and subtropical regions, characterized by endocardial fibrosis, affecting the apices and the inflow tract of the right or left ventricle (or both) and manifesting with a restrictive cardimyopathy and atrioventricular regurgitation leading to severe pulmonary hypertension, very high systemic venous pressure and congestive cardiac failure. Suspected etiologies include helminth and protozoal infestation and malnutrition.

Disease data
Classification

Disease

Synonyms
Davies disease
Choroba Daviesa
TEMF
TEMF
ORPHA code
75565
OMIM code
-
ICD10 code
I42.3
ICD11 code
BC43.20

No additional description.

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