Tropikalne zwłóknienie wsierdzia

Kod Orpha: 75565Kod OMIM:

Definicja

Tropical endomyocardial fibrosis is a restrictive cardiopathy, occuring almost exclusively in children and young adults in tropical and subtropical regions, characterized by endocardial fibrosis, affecting the apices and the inflow tract of the right or left ventricle (or both) and manifesting with a restrictive cardimyopathy and atrioventricular regurgitation leading to severe pulmonary hypertension, very high systemic venous pressure and congestive cardiac failure. Suspected etiologies include helminth and protozoal infestation and malnutrition.

Dane
Klasyfikacja

Choroba

Synonimy
Davies disease
Choroba Daviesa
TEMF
TEMF
Kod ORPHA
75565
Kod OMIM
-
Kod ICD10
I42.3
Kod ICD11
BC43.20

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