Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare primary interstitial lung disease characterized by the accumulation of lipids and proteins related to surfactant in the alveoli in association with the presence of antibodies against granulocyte-macrophage colony-stimulating factor (GM-CSF). The disease leads to a progressive impairment of gas exchange and respiratory insufficiency. Disease data Classification Disease Synonyms Autoimmune PAP aPAP Autoimmunologiczna PAP Idiopatyczna PAP Idiopatyczna proteinoza pęcherzyków płucnych iPAP aPAP ORPHA code 747 OMIM code 610910 ICD10 code J84.0 ICD11 code CB04.31 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl