Norrie disease

Orpha code: 649OMIM code: 310600

Definition

A rare developmental defect during embryogenesis characterized by abnormal retinal development with congenital blindness. Common associated manifestations include sensorineural hearing loss and developmental delay, intellectual disability and/or behavioral disorders.

Disease data
Classification

Malformation syndrome

Synonyms
Atrophia bulborum hereditaria
Choroba Norriego i Warburga
Dziedziczna atrofia opuszkowa
Ślepota Episkopi
Episkopi blindness
Norrie-Warburg disease
ORPHA code
649
OMIM code
310600
ICD10 code
H35.5
ICD11 code
LD21.Y

No additional description.

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