Isolated hyperchlorhidrosis

Orpha code: 542657OMIM code: 143860

Definition

A rare genetic skin disease characterized by excessive salt wasting in sweat, leading to hyponatremic dehydration, hyperkalemia, and poor feeding and slow weight gain in infancy. Laboratory examination shows hyponatremia, hyperkalemia, increased aldosterone, and increased sweat chloride concentrations.

Disease data
Classification

Disease

Synonyms
Carbonic anhydrase XII deficiency
Carbonic anhydrase XII deficiency
ORPHA code
542657
OMIM code
143860
ICD10 code
-
ICD11 code
-

No additional description.

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