Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare large granular lymphocyte leukemia characterized by persistent (> 6 months) natural killer cell lymphocytosis in the absence of clinical diagnosis of leukemia/lymphoma, autoimmune disease, or chronic viral infections. The clinical course is variable, but generally indolent. Patients often remain asymptomatic, or may present with clinical manifestations including vasculitic skin lesions, neutropenic infections, musculoskeletal symptoms, peripheral neuropathy, or splenomegaly. Disease data Classification Disease Synonyms CLPD-NK CNKL CLPD-NK Przewlekła limfocytoza NK Przewlekła limfocytoza z komórek NK Przewlekła choroba limfoproliferacyjna z komórek NK Choroba proliferacyjna limfocytów ziarnistych z linii NK CNKL Chronic NK lymphocytosis Chronic NK-cell lymphocytosis Chronic lymphoproliferative disorder of NK-cells NK-cell lineage granular lymphocyte proliferative disorder ORPHA code 512017 OMIM code - ICD10 code C91.7 ICD11 code 2A90.2 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl