Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare functioning neuroendocrine tumor of pancreas characterized by a typically well-differentiated neoplasm composed of cells expressing serotonin. Patients may present with atypical carcinoid syndrome with abdominal pain, diarrhea, weight loss, and/or flushing. Carcinoid syndrome is usually present only when there are liver metastases. The tumors tend to be larger than non-functioning tumors and are associated with a poorer prognosis because they are almost always metastatic. Disease data Classification Disease Synonyms Serotonin-producing PNET Serotonin-producing pancreatic NET Serotonin-producing pancreatic neuroendocrine tumor Serotonin-producing PNET Serotonin-producing pancreatic NET Serotonin-producing pancreatic neuroendocrine tumor ORPHA code 506090 OMIM code - ICD10 code C25.9 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl