Guz trzustki neuroendokrynny produkujący serotoninę

Kod Orpha: 506090Kod OMIM:

Definicja

A rare functioning neuroendocrine tumor of pancreas characterized by a typically well-differentiated neoplasm composed of cells expressing serotonin. Patients may present with atypical carcinoid syndrome with abdominal pain, diarrhea, weight loss, and/or flushing. Carcinoid syndrome is usually present only when there are liver metastases. The tumors tend to be larger than non-functioning tumors and are associated with a poorer prognosis because they are almost always metastatic.

Dane
Klasyfikacja

Choroba

Synonimy
Serotonin-producing PNET
Serotonin-producing pancreatic NET
Serotonin-producing pancreatic neuroendocrine tumor
Serotonin-producing PNET
Serotonin-producing pancreatic NET
Serotonin-producing pancreatic neuroendocrine tumor
Kod ORPHA
506090
Kod OMIM
-
Kod ICD10
C25.9
Kod ICD11
-

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