DIAPH1-related sensorineural hearing loss-thrombocytopenia syndrome

Orpha code: 494444OMIM code: 124900

Definicja

A rare genetic disease characterized by progressive and severe sensorineural hearing loss with onset in the first decade of life, associated with mild thrombocytopenia, often with enlarged platelets. Most patients do not show significant bleeding tendency.

Disease data
Klasyfikacja

Disease

Synonimy
DIAPH1-related sensorineural deafness-thrombocytopenia syndrome
DIAPH1-related sensorineural deafness-thrombocytopenia syndrome
Kod ORPHA
494444
Kod OMIM
124900
Kod ICD10
H90.3
Kod ICD11
-

No additional description.

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