Omphalomesenteric cyst

Orpha code: 490OMIM code:

Definicja

A rare non-syndromic diaphragmatic or abdominal wall malformation, a remnant of omphalomesenteric duct, characterized by cuboidal or columnar epithelium with gastrointestinal differentiation. Patients may be asymptomatic or present with infraumbilical mass, umbilical lesion with secretions, abdominal pain, hernia, abscess, gastrointestinal tract bleeding, intestinal obstruction, and acute abdomen.

Disease data
Klasyfikacja

Morphological anomaly

Kod ORPHA
490
Kod OMIM
-
Kod ICD10
Q43.0
Kod ICD11
-

No additional description.

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