Omphalomesenteric cyst

Orpha code: 490OMIM code:

Definition

A rare non-syndromic diaphragmatic or abdominal wall malformation, a remnant of omphalomesenteric duct, characterized by cuboidal or columnar epithelium with gastrointestinal differentiation. Patients may be asymptomatic or present with infraumbilical mass, umbilical lesion with secretions, abdominal pain, hernia, abscess, gastrointestinal tract bleeding, intestinal obstruction, and acute abdomen.

Disease data
Classification

Morphological anomaly

ORPHA code
490
OMIM code
-
ICD10 code
Q43.0
ICD11 code
-

No additional description.

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