Microcephaly-congenital cataract-psoriasiform dermatitis syndrome

Orpha code: 488168OMIM code: 616834

Definicja

A rare sterol biosynthesis disorder characterized by microcephaly, bilateral congenital cataract, mild developmental delay, growth delay with short stature, psoriasiform dermatitis of variable severity, and immune dysregulation. Behavioral disorder, joint contractures, and arthralgia have also been described.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
SMO deficiency
Niedobór sterol-C4-metylo oksydazy
Sterol-C4-methyl oxidase deficiency
Kod ORPHA
488168
Kod OMIM
616834
Kod ICD10
E88.8
Kod ICD11
-

No additional description.

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