Fibroblastic rheumatism

Orpha code: 477650OMIM code:

Definicja

A rare rheumatologic disease characterized by sudden onset of symmetric inflammatory distal polyarthritis and multiple firm cutaneous nodules with predilection for the upper and lower extremities. Patients often develop sclerodactyly and joint contractures. Skin biopsy shows fibroblastic proliferation in a matrix of thickened collagen fibers, with loss of elastic fibers and no mucin deposition.

Disease data
Klasyfikacja

Disease

Kod ORPHA
477650
Kod OMIM
-
Kod ICD10
M06.4
Kod ICD11
FB51.3

No additional description.

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