Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare autoimmune bullous skin disease characterized clinically by blistering of the mucous membranes followed by scarring, and immunologically characterized by IgG, IgA and/or C3 deposits on the epidermal basement membrane. The disease principally involves the oral mucosa, but may also affect ocular, pharyngolaryngeal, genital, and esophageal mucous membranes. Disease data Classification Disease Synonyms Cicatricial pemphigoid Cicatricial pemphigoid Mucosynechial pemphigoid Pemfigoid błon śluzowych Mucosal pemphigoid Mucosynechial pemphigoid ORPHA code 46486 OMIM code 164185 ICD10 code L12.1 ICD11 code EB41.1 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl