Mucous membrane pemphigoid

Orpha code: 46486OMIM code: 164185

Definicja

A rare autoimmune bullous skin disease characterized clinically by blistering of the mucous membranes followed by scarring, and immunologically characterized by IgG, IgA and/or C3 deposits on the epidermal basement membrane. The disease principally involves the oral mucosa, but may also affect ocular, pharyngolaryngeal, genital, and esophageal mucous membranes.

Disease data
Klasyfikacja

Disease

Synonimy
Cicatricial pemphigoid
Cicatricial pemphigoid
Mucosynechial pemphigoid
Pemfigoid błon śluzowych
Mucosal pemphigoid
Mucosynechial pemphigoid
Kod ORPHA
46486
Kod OMIM
164185
Kod ICD10
L12.1
Kod ICD11
EB41.1

No additional description.

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