Autosomal recessive brachyolmia

Orpha code: 448242OMIM code: 271630

Definition

Brachyolmia, recessive type is a form of brachyolmia (see this term), a group of rare genetic skeletal disorders, characterized by short-trunked short stature with platyspondyly and scoliosis. Corneal opacities and precocious calcification of the costal cartilage are rare syndromic components. Premature pubarche may occur.

Disease data
Classification

Malformation syndrome

Synonyms
Brachyolmia, Hobaek/Toledo type
Autosomalna recesywna brachyolmia, typ Hobaek/Toledo
ORPHA code
448242
OMIM code
271630
ICD10 code
Q76.3
ICD11 code
-

No additional description.

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