Postural orthostatic tachycardia syndrome due to NET deficiency

Orpha code: 443236OMIM code: 604715

Definition

A rare, genetic, primary orthostatic disorder characterized by dizziness, palpitations, fatigue, blurred vision and tachycardia following postural change from a supine to an upright position, in the absence of hypotension. A syncope with transient cognitive impairment and dyspnea may also occur. The norepinephrine transporter deficiency leads to abnormal uptake and high plasma concentrations of norepinephrine.

Disease data
Classification

Disease

Synonyms
Familial orthostatic tachycardia due to norepinephrine transporter deficiency
Rodzinny częstoskurcz ortostatyczny spowodowany niedoborem transportera norepinefryny
Zespół częstoskurczu posturalnego spowodowanego niedoborem NET
Orthostatic intolerance due to NET deficiency
POTS due to NET deficiency
ORPHA code
443236
OMIM code
604715
ICD10 code
I95.1
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl