Isolated agenesis of gallbladder

Orpha code: 440987OMIM code:

Definition

A rare biliary tract disease characterized by congenital absence of the gallbladder and cystic duct. The majority of patients are asymptomatic. Possible clinical manifestations include abdominal pain and tenderness in the right upper quadrant, nausea, vomiting, fatty food intolerance, and jaundice. Frequency of choledocholithiasis is increased significantly.

Disease data
Classification

Morphological anomaly

ORPHA code
440987
OMIM code
-
ICD10 code
Q44.0
ICD11 code
LB20.10

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl