Isolated sedoheptulokinase deficiency

Orpha code: 440713OMIM code: 617213

Definition

A rare, hereditary disorder of pentose phosphate metabolism characterized by increased urine levels of sedoheptulose and erythritol, and low-to-normal excretion of sedoheptulose-7P. Clinical presentation of this disorder is currently unclear.

Disease data
Classification

Disease

Synonyms
Isolated SHPK deficiency
Izolowany Niedobór SHPK
ORPHA code
440713
OMIM code
617213
ICD10 code
E88.8
ICD11 code
-

No additional description.

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