Spinocerebellar ataxia type 40

Orpha code: 423275OMIM code: 616053

Definition

Spinocerebellar ataxia type 40 (SCA40) is a very rare subtype of autosomal dominant cerebellar ataxia type 1, characterized by the adult-onset of unsteady gait and dysarthria, followed by wide-based gait, gait ataxia, ocular dysmetria, intention tremor, scanning speech, hyperreflexia and dysdiadochokinesis.

Disease data
Classification

Disease

Synonyms
SCA40
SCA40
ORPHA code
423275
OMIM code
616053
ICD10 code
G11.8
ICD11 code
-

No additional description.

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