13q12.3 microdeletion syndrome

Orpha code: 412035OMIM code:

Definition

13q12.3 microdeletion syndrome is a rare chromosomal anomaly characterized by moderate intellectual disability, speech delay, postnatal microcephaly, eczema or atopic dermatitis, characteristic facial features (malar flattening, prominent nose, underdeveloped alae nasi, smooth philtrum, and thin vermillion of the upper lip), and reduced sensitivity to pain.

Disease data
Classification

Malformation syndrome

Synonyms
Del(13)(q12.3)
Del(13)(q12.3)
Monosomia 13q12.3
Monosomy 13q12.3
ORPHA code
412035
OMIM code
-
ICD10 code
Q93.5
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl