Early-onset epileptic encephalopathy-cortical blindness-intellectual disability-facial dysmorphism syndrome

Orpha code: 411986OMIM code: 615859

Definition

Early-onset epileptic encephalopathy-cortical blindness-intellectual disability-facial dysmorphism syndrome is a rare, syndromic intellectual disability syndrome characterized by cortical blindness, different types of seizures, intellectual disability with limited or absent speech, and dysmorphic facial features. Brain imaging typically shows mild pontine hypoplasia, hypoplasia of the corpus callosum and atrophy in the occipital region.

Disease data
Classification

Malformation syndrome

Synonyms
Epilepsy-cortical blindness-intellectual disability-facial dysmorphism syndrome
Zespół padaczka ślepota korowa-niepełnosprawność intelektualna-dysmorfia twarzy
ORPHA code
411986
OMIM code
615859
ICD10 code
G40.4
ICD11 code
-

No additional description.

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