Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A rare ovarian germ cell tumor characterized by a unilateral large adnexal mass containing variable amounts of immature embryonal-type tissues (mostly in the form of neuroectodermal tubules and rosettes, sometimes with a component of cellular mitotically active glia), admixed with ectodermal and endodermal elements with varying degrees of maturation. Patients typically present in their first three decades of life with signs and symptoms related to mass effect. The tumor is often associated with the occurrence of innumerable miliary nodules of mature glia in the peritoneum (gliomatosis peritonei) and abdominal lymph nodes. Disease data Klasyfikacja Disease Synonimy Immature teratoma of ovary Niezróżnicowana teratoma jajników Złośliwa teratoma jajników Potworniak niedojrzały jajnika Ovarian immature teratoma Ovarian malignant teratoma Kod ORPHA 398987 Kod OMIM - Kod ICD10 C56 Kod ICD11 2C73.3 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl