Złośliwy potworniak jajnika

Kod Orpha: 398987Kod OMIM:

Definicja

A rare ovarian germ cell tumor characterized by a unilateral large adnexal mass containing variable amounts of immature embryonal-type tissues (mostly in the form of neuroectodermal tubules and rosettes, sometimes with a component of cellular mitotically active glia), admixed with ectodermal and endodermal elements with varying degrees of maturation. Patients typically present in their first three decades of life with signs and symptoms related to mass effect. The tumor is often associated with the occurrence of innumerable miliary nodules of mature glia in the peritoneum (gliomatosis peritonei) and abdominal lymph nodes.

Dane
Klasyfikacja

Choroba

Synonimy
Immature teratoma of ovary
Niezróżnicowana teratoma jajników
Złośliwa teratoma jajników
Potworniak niedojrzały jajnika
Ovarian immature teratoma
Ovarian malignant teratoma
Kod ORPHA
398987
Kod OMIM
-
Kod ICD10
C56
Kod ICD11
2C73.3

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