Neonatal antiphospholipid syndrome

Orpha code: 398097OMIM code:

Definition

Neonatal antiphospholipid syndrome is a rare, secondary, neonatal autoimmune disease characterized by single or recurrent episodes of venous, arterial or mixed thrombosis in a neonate whose mother does not have antiphospholipid syndrome manifestations. Patients present positive antiphospholipid antibodies and may have additional abnormalities associated (e.g. cardiac valve disease, livedo reticularis, thrombocytopenia, nephropathy, neurological manifestations).

Disease data
Classification

Disease

Synonyms
Neonatal Hughes syndrome
APS noworodkowa
Zespół Hughesa noworodków
Zespół przeciwciał antyfosfolipidowych noworodków
Neonatal antiphospholipid antibody syndrome
ORPHA code
398097
OMIM code
-
ICD10 code
D68.6
ICD11 code
-

No additional description.

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